Reverse LMA insertion in a neonate with Klippel-Feil syndrome--case report.

نویسنده

  • Tariq Al Zahrani
چکیده

Klippel-Feil syndrome (KFS) was first described by Maurice Klippel and Andre Feil in 1912 in a patient with congenital fusion of cervical vertebrae. KFS is a complex syndrome of osseous and visceral anomalies that include the classical clinical triad of short neck, limitation of head and neck movements and low posterior hairline. It is associated with several defects, such as deafness, either conductive or neural, congenital heart defects, the most common being a ventricular septal defect, mental deficiency, cleft palate, rib defects, the sprengel sequence (elevated scapula), and scoliosis. Patients with KFS exhibit a smaller lower third of the face and facial asymmetry with no dental implications. KFS occurs in 1 of every 42,000 births, and 60% of cases are in females.

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منابع مشابه

One Case of Klippel-Fiel Syndrome

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Klippel-Feil syndrome: a case report.

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عنوان ژورنال:
  • Middle East journal of anaesthesiology

دوره 19 3  شماره 

صفحات  -

تاریخ انتشار 2007